Eosinophilic Granulomatosis With Polyangiitis (Churg Strauss Syndrome): Case Report

Yıl 2016, Cilt: 13 Sayı: 1, 84 - 87, 28.04.2016

Hakan Tanrıverdi Fırat Uygur Bülent Altınsoy , Fatma Erboy , Ömer Yazgan Figen Atalay

Öz

Eosinophilic granulomatosis with polyangiitis (EGPA) is a systemic necrotizing vasculitis characterized by
tissue and blood eosinophilia. Several drugs including leukotriene receptor antagonists (LTRAs) are
suspected to trigger EGPAdevelopment. Here, we present a case of EGPAunrelated to LTRAs.

Anahtar Kelimeler

Eosinophilia, Leukotriene Receptor Antagonists, Eosinophilic Granulomatous, Vasculitis

Polianjitisle Seyreden Eozinofilik Granülomatozis (Churg Strauss Sendromu): Olgu Sunumu

Öz

Polianjitisle birlikte seyreden eozinofilik granülomatozis (Churg Strauss sendromu), nadir, sıklıkla solunum
sistemini tutan ve özellikle küçük ve orta çaplı damarları etkileyen, astım ve doku eozinofilisi ile karakterize,
sistemik nekrotizan bir vaskülittir. Lökotrien antagonistlerini de içeren pek çok ilacın bu hastalığın
gelişiminde rolü olduğundan şüphelenilmektedir. Biz de klinik ve radyolojik bulgularla tanı alan ve lökotrien
reseptör antagonistleri ile ilişkili olmadığını düşündüğümüz bir olguyu sunmak istedik. 

Anahtar Kelimeler

Eozinofili, lökotrien reseptör antagonisti, eozinofilik granülamatöz, Vaskülit

Kaynakça

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