Cantrell’s pentalogy

Öz

Pentalogy of Cantrell is a rare congenital malformation. It’s composed of defects of lower sternum, anterior diaphgram, midline supraumbilical abdominal wall, diaphragmatic pericardium with ectopia cordis. In this article we discussed Cantrell’s pentalogy with the literature findings.

Anahtar Kelimeler

• Cantrell’s pentalogy,abdominal wall defects ( omphalocele ),ectopia cordis

Cantrell Pentalojisi

Öz

Cantrell pentalojisi oldukça nadir görülen ve orta hat supraumbilikal abdominal defekt, sternum alt uç defekti, diafragma ön kısmında defekt, perikardın diafragma yüzünün eksikliği ve intrakardiak anomaliler ile karakterize bir sendromdur. Az görülen bir anomaliler grubu olması nedeniyle ilgili literatür gözden geçirilerek olgumuza ait özellikler sunulmuştur.

Anahtar Kelimeler

• Cantrell pentalojisi,abdominal duvar defekti ( omfalosel),ektopia kordis

Kaynakça

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